KUMJ | VOL. 23 | NO. 2 | ISSUE 90 | APRIL - JUNE, 2025

Non-necrotising Scleritis and Spherophakia in Marfan Syndrome: A Rare Situation Adhering to Hickam’s Dictum
Parajuli S, Sharma S, Shrestha R, Chapagain S

Abstract:
Marfan syndrome is an autosomal dominant, connective tissue disorder that affects various systems of the body including the eyes. We present a case of a 22 year old man with Marfan syndrome presented with a painful red left eye. On examination he was diagnosed to have non-necrotising scleritis and microspherophakia. Non-necrotising scleritis with microspherophakia is a rare and arduous situation. This is an interesting case where Hickam’s dictum prevails over its counter argument of Occam’s razor principle.
Keyword : Marfan syndrome, Non-necrotising scleritis, Spherophakia